Contributor: Gordon K. Klintworth
Spinocerebellar ataxia (spinocerebellar degeneration) is a heterogeneous inherited degenerative disorder of the central nervous system that involves neurons in the cerebellum, olives in the brain stem and tracts in the spinal cord associated with ataxia. Sixteen types have been identified: spinocerebellar ataxia 1, spinocerebellar ataxia 2, spinocerebellar ataxia 3, spinocerebellar ataxia 4, spinocerebellar ataxia 5, spinocerebellar ataxia 6, spinocerebellar ataxia 7, spinocerebellar ataxia 8, spinocerebellar ataxia 9, spinocerebellar ataxia 10, spinocerebellar ataxia 11, spinocerebellar ataxia 12, spinocerebellar ataxia 13, spinocerebellar ataxia 14, spinocerebellar ataxia 15, and spinocerebellar ataxia 16.